CCDC103 Antibody

文獻引用 (1) 說明書

產品詳情

產品名稱：

Rabbit anti-Homo sapiens (Human) CCDC103 Polyclonal antibody
Uniprot No.：

Q8IW40
基因名：

CCDC103
別名：

CCDC103Coiled-coil domain-containing protein 103 antibody
宿主：

Rabbit
反應種屬：

Human, Mouse
免疫原：

Recombinant Human Coiled-coil domain-containing protein 103 protein (1-242AA)
免疫原種屬：

Homo sapiens (Human)

標記方式：

Non-conjugated

本頁面中的產品，CCDC103 Antibody (CSB-PA812877LA01HU)，的標記方式是Non-conjugated。對于CCDC103 Antibody，我們還提供其他標記。見下表：

標記方式	貨號	產品名稱	應用
HRP	CSB-PA812877LB01HU	CCDC103 Antibody, HRP conjugated	ELISA
FITC	CSB-PA812877LC01HU	CCDC103 Antibody, FITC conjugated
Biotin	CSB-PA812877LD01HU	CCDC103 Antibody, Biotin conjugated	ELISA

克隆類型：

Polyclonal
抗體亞型：

IgG
純化方式：

>95%, Protein G purified
濃度：

It differs from different batches. Please contact us to confirm it.
保存緩沖液：

Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
產品提供形式：

Liquid
應用范圍：

ELISA, WB

推薦稀釋比：

Application	Recommended Dilution
WB	1:1000-1:5000

Protocols：

ELISA Protocol
Western Blotting (WB) Protocol
儲存條件：

Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
貨期：

Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
用途：

For Research Use Only. Not for use in diagnostic or therapeutic procedures.

功能：

Dynein-attachment factor required for cilia motility.
基因功能參考文獻：
1. The CCDC103 p.His154Pro mutation is more prevalent than previously thought in the South Asian community in the UK and causes primary ciliary dyskinesia that can be difficult to diagnose using pathology-based clinical tests. PMID: 28790179
2. A variable and complex phenotype caused by the co-inheritance of a single gene mutation in CCDC103 and a microduplication at 17q12, both on chromosome 17. PMID: 26123568
3. These results identify Ccdc103 as a dynein arm attachment factor that causes primary ciliary dyskinesia when mutated. PMID: 22581229
相關疾病：

Ciliary dyskinesia, primary, 17 (CILD17)
亞細胞定位：

Cytoplasm. Cell projection, cilium, flagellum.
蛋白家族：

CCDC103/PR46b family
數據庫鏈接：

HGNC: 32700

OMIM: 614677

KEGG: hsa:388389

STRING: 9606.ENSP00000387252

UniGene: Hs.743398

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